2 Cases of Werner's Syndrome with Metabolic Disturbance: Hyperlipidemia and Hyperinsulinism

Hyungin Chi, Masutaka Furue, Iwao Ando, Fujio Otsuka, Yasumasa Ishibashi, Kuniaki Ohara, Hiroko Nanko

Research output: Contribution to journalArticlepeer-review

Abstract

We have experienced 2 cases of Werner's syndrome with typical clinical features and metabolic disturbances. In case 1, plasma lipoprotein analysis revealed hyperlipidemia with increased triglyceride rich lipoproteins, such as chylomicron, or very low density lipoprotein. However, the low density lipoprotein was decreased. Case 2 suffered from latent diabetes with hyperinsulinism. However, insuline tolerance test and plasma levels of C-peptide were within normal limits. Metabolic disturbances in Werner's syndrome were discussed including reference to a previous survey.

Original languageEnglish
Pages (from-to)824-828
Number of pages5
JournalNishi Nihon Hifuka
Volume50
Issue number5
DOIs
Publication statusPublished - 1988
Externally publishedYes

All Science Journal Classification (ASJC) codes

  • Dermatology

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