A case of progressive hemifacial atrophy with Pourfour de Petit syndrome which was successfully treated by stellate ganglion block

Yuji Kawano, Eiichi Araki, Kenji Arakawa, Syouji Matsumono, Takeshi Yamada, Jun-Ichi Kira

Research output: Contribution to journalArticle

7 Citations (Scopus)

Abstract

We herein report a 31-year-old woman with progressive hemifacial atrophy. The atrophy at her left face began about ten years ago. She had been in a traffic accident one year before the onset of her facial atrophy. Neurological examination revealed anisocoria (right < left) and retraction of the left eyelid, which thus suggested the presence of Pourfour de Petit syndrome. The pupillary reaction to both cocaine and tyramine were reduced bilaterally. Thermography of the face showed slightly lower surface temperature on the left side. A facial thermal sweat test was normal. These findings indicated local hyperactivity of the sympathetic nervous system at the Th1-Th2 levels on the left side. A left stellate ganglion block effectively induced an accumulation of the subcutaneous tissue of her face on the left side. This is a very rare case in which local sympathetic hyperactivity is present and has caused progressive hemifacial atrophy.

Original languageEnglish
Pages (from-to)731-734
Number of pages4
JournalClinical Neurology
Volume39
Issue number7
Publication statusPublished - Jul 1 1999

Fingerprint

Facial Hemiatrophy
Stellate Ganglion
Atrophy
Anisocoria
Tyramine
Sweat
Traffic Accidents
Sympathetic Nervous System
Subcutaneous Tissue
Neurologic Examination
Eyelids
Cocaine
Hot Temperature
Temperature

All Science Journal Classification (ASJC) codes

  • Clinical Neurology

Cite this

A case of progressive hemifacial atrophy with Pourfour de Petit syndrome which was successfully treated by stellate ganglion block. / Kawano, Yuji; Araki, Eiichi; Arakawa, Kenji; Matsumono, Syouji; Yamada, Takeshi; Kira, Jun-Ichi.

In: Clinical Neurology, Vol. 39, No. 7, 01.07.1999, p. 731-734.

Research output: Contribution to journalArticle

Kawano, Yuji ; Araki, Eiichi ; Arakawa, Kenji ; Matsumono, Syouji ; Yamada, Takeshi ; Kira, Jun-Ichi. / A case of progressive hemifacial atrophy with Pourfour de Petit syndrome which was successfully treated by stellate ganglion block. In: Clinical Neurology. 1999 ; Vol. 39, No. 7. pp. 731-734.
@article{ebe0162c933245509057861058293e62,
title = "A case of progressive hemifacial atrophy with Pourfour de Petit syndrome which was successfully treated by stellate ganglion block",
abstract = "We herein report a 31-year-old woman with progressive hemifacial atrophy. The atrophy at her left face began about ten years ago. She had been in a traffic accident one year before the onset of her facial atrophy. Neurological examination revealed anisocoria (right < left) and retraction of the left eyelid, which thus suggested the presence of Pourfour de Petit syndrome. The pupillary reaction to both cocaine and tyramine were reduced bilaterally. Thermography of the face showed slightly lower surface temperature on the left side. A facial thermal sweat test was normal. These findings indicated local hyperactivity of the sympathetic nervous system at the Th1-Th2 levels on the left side. A left stellate ganglion block effectively induced an accumulation of the subcutaneous tissue of her face on the left side. This is a very rare case in which local sympathetic hyperactivity is present and has caused progressive hemifacial atrophy.",
author = "Yuji Kawano and Eiichi Araki and Kenji Arakawa and Syouji Matsumono and Takeshi Yamada and Jun-Ichi Kira",
year = "1999",
month = "7",
day = "1",
language = "English",
volume = "39",
pages = "731--734",
journal = "Clinical Neurology",
issn = "0009-918X",
publisher = "Societas Neurologica Japonica",
number = "7",

}

TY - JOUR

T1 - A case of progressive hemifacial atrophy with Pourfour de Petit syndrome which was successfully treated by stellate ganglion block

AU - Kawano, Yuji

AU - Araki, Eiichi

AU - Arakawa, Kenji

AU - Matsumono, Syouji

AU - Yamada, Takeshi

AU - Kira, Jun-Ichi

PY - 1999/7/1

Y1 - 1999/7/1

N2 - We herein report a 31-year-old woman with progressive hemifacial atrophy. The atrophy at her left face began about ten years ago. She had been in a traffic accident one year before the onset of her facial atrophy. Neurological examination revealed anisocoria (right < left) and retraction of the left eyelid, which thus suggested the presence of Pourfour de Petit syndrome. The pupillary reaction to both cocaine and tyramine were reduced bilaterally. Thermography of the face showed slightly lower surface temperature on the left side. A facial thermal sweat test was normal. These findings indicated local hyperactivity of the sympathetic nervous system at the Th1-Th2 levels on the left side. A left stellate ganglion block effectively induced an accumulation of the subcutaneous tissue of her face on the left side. This is a very rare case in which local sympathetic hyperactivity is present and has caused progressive hemifacial atrophy.

AB - We herein report a 31-year-old woman with progressive hemifacial atrophy. The atrophy at her left face began about ten years ago. She had been in a traffic accident one year before the onset of her facial atrophy. Neurological examination revealed anisocoria (right < left) and retraction of the left eyelid, which thus suggested the presence of Pourfour de Petit syndrome. The pupillary reaction to both cocaine and tyramine were reduced bilaterally. Thermography of the face showed slightly lower surface temperature on the left side. A facial thermal sweat test was normal. These findings indicated local hyperactivity of the sympathetic nervous system at the Th1-Th2 levels on the left side. A left stellate ganglion block effectively induced an accumulation of the subcutaneous tissue of her face on the left side. This is a very rare case in which local sympathetic hyperactivity is present and has caused progressive hemifacial atrophy.

UR - http://www.scopus.com/inward/record.url?scp=0032708261&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=0032708261&partnerID=8YFLogxK

M3 - Article

C2 - 10548911

AN - SCOPUS:0032708261

VL - 39

SP - 731

EP - 734

JO - Clinical Neurology

JF - Clinical Neurology

SN - 0009-918X

IS - 7

ER -