An adult case with hunter's syndrome presenting prominent hepatic failure: Light and electron microscopic features of the liver

Tsuyoshi Yoshimoto, Makoto Nakamuta, Kazuhiro Kotoh, Motoyuki Kohjima, Shusuke Morizono, Yuzuru Miyagi, Hironori Sakai, Munechika Enjoji

Research output: Contribution to journalArticle

4 Citations (Scopus)

Abstract

We describe a 40-year-old male patient with Hunter's syndrome. His main manifestations were ascites and esophageal varices due to cirrhotic liver. We obtained hepatic biopsy samples and examined them. Ultrastructurally, the features of the hepatocytes and Kupffer cells were the same as those reported in young patients. The passage of 40 years led to gradual progression to fibrosis, and ultimately liver cirrhosis. Namely, with a longer survival time, the complications of liver cirrhosis become more remarkable. Hepatic fibrosis in Hunter's syndrome is slowly progressive and patients who are expected to have a longer life span should be continuously monitored for hepatic complications.

Original languageEnglish
Pages (from-to)1133-1135
Number of pages3
JournalInternal Medicine
Volume45
Issue number20
DOIs
Publication statusPublished - Nov 15 2006

All Science Journal Classification (ASJC) codes

  • Internal Medicine

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