Anesthetic management of a patient with Williams syndrome

Research output: Contribution to journalArticle

Abstract

A 9-year-old boy with Williams syndrome was scheduled to receive dental treatment under general anesthesia. He had been diagnosed as having Williams syndrome based on the presence of characteristic features, including an elfin face, mental retardation, and congenital supravalvular aortic stenosis and hypercalcemia. Airway management using a mask technique was easily performed. Anesthesia was induced slowly with the inhalation of oxygen and sevoflurane. After obtaining an intravenous route, fentanyl and rocuronium were administered and the patient was intubated nasally. Tracheal intubation (using an Airway Scope®) was performed. The anesthesia was safely maintained using sevoflurane. Patients with Williams syndrome have a high risk of sudden death caused by arrhythmias or cardiac arrest. Therefore, special care to prevent heart failure during the perioperative period using a noninvasive hemodynamic monitor and appropriate management of the circulatory system, mental retardation, malignant hyperthermia, and hypercalcemia is needed in patients with this syndrome.

Original languageEnglish
Pages (from-to)150-152
Number of pages3
JournalJournal of Japanese Dental Society of Anesthesiology
Volume44
Issue number2
Publication statusPublished - 2016

Fingerprint

Williams Syndrome
Anesthetics
Hypercalcemia
Intellectual Disability
Anesthesia
Supravalvular Aortic Stenosis
Malignant Hyperthermia
Perioperative Period
Airway Management
Fentanyl
Masks
Cardiovascular System
Sudden Death
Heart Arrest
Intubation
General Anesthesia
Inhalation
Cardiac Arrhythmias
Tooth
Heart Failure

All Science Journal Classification (ASJC) codes

  • Anesthesiology and Pain Medicine
  • Dentistry(all)

Cite this

Anesthetic management of a patient with Williams syndrome. / Hitosugi, Takashi; Tsukamoto, Masanori; Shiba, Rika; Koyama, Sayuri; Yokoyama, Takeshi.

In: Journal of Japanese Dental Society of Anesthesiology, Vol. 44, No. 2, 2016, p. 150-152.

Research output: Contribution to journalArticle

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