Double lumbosacral lipomas of the dorsal and filar types associated with OEIS complex - Case report

So Tokunaga, Takato Morioka, Kimiaki Hashiguchi, Kazuhiro Samura, Fumiaki Yoshida, Yasushi Miyagi, Takashi Yoshiura, Takeshi Yamanouchi, Tomio Sasaki

Research output: Contribution to journalArticlepeer-review

9 Citations (Scopus)

Abstract

A female baby was born at 37 weeks and 6 days gestation by vaginal delivery with omphalocele, exstrophy of the cloaca, and imperforate anus, indicating the presence of OEIS complex, a rare combination of defects consisting of omphalocele (O), exstrophy of the cloaca (E), imperforate anus (I), and spinal deformity (S), associated with lumbosacral lipoma. The most common associated spinal deformity is terminal myelocystocele, and spinal lipoma is rare. Constructive interference in steady-state magnetic resonance imaging clearly revealed double lipomas, a dorsal-type lipoma, located dorsal to the lowlying conus medullaris, and a filar-type lipoma, revealed by a thickened and fatty filum terminale. After recovery from abdominogenital repairs, debulking of the dorsal-type lipoma and untethering of the spinal cord by sectioning of the filar-type lipoma were performed at the age of 14 months. Neurosurgical treatment for occult spinal dysraphism should be undertaken after recovery from the initial series of major abdominogenital procedures.

Original languageEnglish
Pages (from-to)487-490
Number of pages4
JournalNeurologia medico-chirurgica
Volume49
Issue number10
DOIs
Publication statusPublished - 2009

All Science Journal Classification (ASJC) codes

  • Surgery
  • Clinical Neurology

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