Abstract
A female baby was born at 37 weeks and 6 days gestation by vaginal delivery with omphalocele, exstrophy of the cloaca, and imperforate anus, indicating the presence of OEIS complex, a rare combination of defects consisting of omphalocele (O), exstrophy of the cloaca (E), imperforate anus (I), and spinal deformity (S), associated with lumbosacral lipoma. The most common associated spinal deformity is terminal myelocystocele, and spinal lipoma is rare. Constructive interference in steady-state magnetic resonance imaging clearly revealed double lipomas, a dorsal-type lipoma, located dorsal to the lowlying conus medullaris, and a filar-type lipoma, revealed by a thickened and fatty filum terminale. After recovery from abdominogenital repairs, debulking of the dorsal-type lipoma and untethering of the spinal cord by sectioning of the filar-type lipoma were performed at the age of 14 months. Neurosurgical treatment for occult spinal dysraphism should be undertaken after recovery from the initial series of major abdominogenital procedures.
| Original language | English |
|---|---|
| Pages (from-to) | 487-490 |
| Number of pages | 4 |
| Journal | Neurologia medico-chirurgica |
| Volume | 49 |
| Issue number | 10 |
| DOIs | |
| Publication status | Published - Dec 1 2009 |
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All Science Journal Classification (ASJC) codes
- Surgery
- Clinical Neurology
Cite this
Double lumbosacral lipomas of the dorsal and filar types associated with OEIS complex - Case report. / Tokunaga, So; Morioka, Takato; Hashiguchi, Kimiaki; Samura, Kazuhiro; Yoshida, Fumiaki; Miyagi, Yasushi; Yoshiura, Takashi; Yamanouchi, Takeshi; Sasaki, Tomio.
In: Neurologia medico-chirurgica, Vol. 49, No. 10, 01.12.2009, p. 487-490.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Double lumbosacral lipomas of the dorsal and filar types associated with OEIS complex - Case report
AU - Tokunaga, So
AU - Morioka, Takato
AU - Hashiguchi, Kimiaki
AU - Samura, Kazuhiro
AU - Yoshida, Fumiaki
AU - Miyagi, Yasushi
AU - Yoshiura, Takashi
AU - Yamanouchi, Takeshi
AU - Sasaki, Tomio
PY - 2009/12/1
Y1 - 2009/12/1
N2 - A female baby was born at 37 weeks and 6 days gestation by vaginal delivery with omphalocele, exstrophy of the cloaca, and imperforate anus, indicating the presence of OEIS complex, a rare combination of defects consisting of omphalocele (O), exstrophy of the cloaca (E), imperforate anus (I), and spinal deformity (S), associated with lumbosacral lipoma. The most common associated spinal deformity is terminal myelocystocele, and spinal lipoma is rare. Constructive interference in steady-state magnetic resonance imaging clearly revealed double lipomas, a dorsal-type lipoma, located dorsal to the lowlying conus medullaris, and a filar-type lipoma, revealed by a thickened and fatty filum terminale. After recovery from abdominogenital repairs, debulking of the dorsal-type lipoma and untethering of the spinal cord by sectioning of the filar-type lipoma were performed at the age of 14 months. Neurosurgical treatment for occult spinal dysraphism should be undertaken after recovery from the initial series of major abdominogenital procedures.
AB - A female baby was born at 37 weeks and 6 days gestation by vaginal delivery with omphalocele, exstrophy of the cloaca, and imperforate anus, indicating the presence of OEIS complex, a rare combination of defects consisting of omphalocele (O), exstrophy of the cloaca (E), imperforate anus (I), and spinal deformity (S), associated with lumbosacral lipoma. The most common associated spinal deformity is terminal myelocystocele, and spinal lipoma is rare. Constructive interference in steady-state magnetic resonance imaging clearly revealed double lipomas, a dorsal-type lipoma, located dorsal to the lowlying conus medullaris, and a filar-type lipoma, revealed by a thickened and fatty filum terminale. After recovery from abdominogenital repairs, debulking of the dorsal-type lipoma and untethering of the spinal cord by sectioning of the filar-type lipoma were performed at the age of 14 months. Neurosurgical treatment for occult spinal dysraphism should be undertaken after recovery from the initial series of major abdominogenital procedures.
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UR - http://www.scopus.com/inward/citedby.url?scp=70549106479&partnerID=8YFLogxK
U2 - 10.2176/nmc.49.487
DO - 10.2176/nmc.49.487
M3 - Article
C2 - 19855150
AN - SCOPUS:70549106479
VL - 49
SP - 487
EP - 490
JO - Neurologia Medico-Chirurgica
JF - Neurologia Medico-Chirurgica
SN - 0470-8105
IS - 10
ER -