General anesthesia for a patient with cornelia de lange syndrome

Takeshi Yokoyama, Miho Tomoda, Tomoki Nishiyama, Takako Matsuda, Shoji Fujimoto, Kazuo Hanaoka, Masanobu Manabe

Research output: Contribution to journalArticle

9 Citations (Scopus)

Abstract

Cornelia de Lange syndrome involves anomalies in cardio-vascular and musculo-skeletal systems, and mental retardation. In addition, a patient with this syndrome shows a peculiar look. A 22-year-old woman with Cornelia de Lange syndrome underwent general anesthesia twice. She has a small mouth, thin lips, a short neck, short limbs, and stiffness of the neck and some joints associated with slight mental retardation. She was scheduled for arthroscopy and then for rotational acetabular osteotomy and valgus osteotomy. The maximum distance between the upper and lower incisors was 34 mm, when she opened her mouth. Anesthesia was induced with sevoflurane increased slowly to 7.0% in oxygen 6 l · min-1 in both procedures. After the administration of 4% lidocaine 3.5ml into the pharynx, orotracheal intubation was attempted, but was not successful. Then blind naso-tracheal intubation was performed successfuly under spontaneous respiration under sevoflurane-oxygen inhalation. The induction of anesthesia with sevoflurane under spontaneous respiration was useful for blind naso-tracheal intubation in a case with difficult intubation such as in Cornelia de Lange syndrome.

Original languageEnglish
Pages (from-to)786-787
Number of pages2
JournalJapanese Journal of Anesthesiology
Volume49
Issue number7
Publication statusPublished - Dec 1 2000
Externally publishedYes

Fingerprint

De Lange Syndrome
Intubation
General Anesthesia
Osteotomy
Intellectual Disability
Mouth
Respiration
Neck
Anesthesia
Oxygen
Arthroscopy
Incisor
Lip
Lidocaine
Pharynx
Inhalation
Blood Vessels
Extremities
Joints
sevoflurane

All Science Journal Classification (ASJC) codes

  • Anesthesiology and Pain Medicine

Cite this

Yokoyama, T., Tomoda, M., Nishiyama, T., Matsuda, T., Fujimoto, S., Hanaoka, K., & Manabe, M. (2000). General anesthesia for a patient with cornelia de lange syndrome. Japanese Journal of Anesthesiology, 49(7), 786-787.

General anesthesia for a patient with cornelia de lange syndrome. / Yokoyama, Takeshi; Tomoda, Miho; Nishiyama, Tomoki; Matsuda, Takako; Fujimoto, Shoji; Hanaoka, Kazuo; Manabe, Masanobu.

In: Japanese Journal of Anesthesiology, Vol. 49, No. 7, 01.12.2000, p. 786-787.

Research output: Contribution to journalArticle

Yokoyama, T, Tomoda, M, Nishiyama, T, Matsuda, T, Fujimoto, S, Hanaoka, K & Manabe, M 2000, 'General anesthesia for a patient with cornelia de lange syndrome', Japanese Journal of Anesthesiology, vol. 49, no. 7, pp. 786-787.
Yokoyama T, Tomoda M, Nishiyama T, Matsuda T, Fujimoto S, Hanaoka K et al. General anesthesia for a patient with cornelia de lange syndrome. Japanese Journal of Anesthesiology. 2000 Dec 1;49(7):786-787.
Yokoyama, Takeshi ; Tomoda, Miho ; Nishiyama, Tomoki ; Matsuda, Takako ; Fujimoto, Shoji ; Hanaoka, Kazuo ; Manabe, Masanobu. / General anesthesia for a patient with cornelia de lange syndrome. In: Japanese Journal of Anesthesiology. 2000 ; Vol. 49, No. 7. pp. 786-787.
@article{633acf7ff97742eb81604cfb0be32566,
title = "General anesthesia for a patient with cornelia de lange syndrome",
abstract = "Cornelia de Lange syndrome involves anomalies in cardio-vascular and musculo-skeletal systems, and mental retardation. In addition, a patient with this syndrome shows a peculiar look. A 22-year-old woman with Cornelia de Lange syndrome underwent general anesthesia twice. She has a small mouth, thin lips, a short neck, short limbs, and stiffness of the neck and some joints associated with slight mental retardation. She was scheduled for arthroscopy and then for rotational acetabular osteotomy and valgus osteotomy. The maximum distance between the upper and lower incisors was 34 mm, when she opened her mouth. Anesthesia was induced with sevoflurane increased slowly to 7.0{\%} in oxygen 6 l · min-1 in both procedures. After the administration of 4{\%} lidocaine 3.5ml into the pharynx, orotracheal intubation was attempted, but was not successful. Then blind naso-tracheal intubation was performed successfuly under spontaneous respiration under sevoflurane-oxygen inhalation. The induction of anesthesia with sevoflurane under spontaneous respiration was useful for blind naso-tracheal intubation in a case with difficult intubation such as in Cornelia de Lange syndrome.",
author = "Takeshi Yokoyama and Miho Tomoda and Tomoki Nishiyama and Takako Matsuda and Shoji Fujimoto and Kazuo Hanaoka and Masanobu Manabe",
year = "2000",
month = "12",
day = "1",
language = "English",
volume = "49",
pages = "786--787",
journal = "Japanese Journal of Anesthesiology",
issn = "0021-4892",
publisher = "Kokuseido Publishing Co. Ltd",
number = "7",

}

TY - JOUR

T1 - General anesthesia for a patient with cornelia de lange syndrome

AU - Yokoyama, Takeshi

AU - Tomoda, Miho

AU - Nishiyama, Tomoki

AU - Matsuda, Takako

AU - Fujimoto, Shoji

AU - Hanaoka, Kazuo

AU - Manabe, Masanobu

PY - 2000/12/1

Y1 - 2000/12/1

N2 - Cornelia de Lange syndrome involves anomalies in cardio-vascular and musculo-skeletal systems, and mental retardation. In addition, a patient with this syndrome shows a peculiar look. A 22-year-old woman with Cornelia de Lange syndrome underwent general anesthesia twice. She has a small mouth, thin lips, a short neck, short limbs, and stiffness of the neck and some joints associated with slight mental retardation. She was scheduled for arthroscopy and then for rotational acetabular osteotomy and valgus osteotomy. The maximum distance between the upper and lower incisors was 34 mm, when she opened her mouth. Anesthesia was induced with sevoflurane increased slowly to 7.0% in oxygen 6 l · min-1 in both procedures. After the administration of 4% lidocaine 3.5ml into the pharynx, orotracheal intubation was attempted, but was not successful. Then blind naso-tracheal intubation was performed successfuly under spontaneous respiration under sevoflurane-oxygen inhalation. The induction of anesthesia with sevoflurane under spontaneous respiration was useful for blind naso-tracheal intubation in a case with difficult intubation such as in Cornelia de Lange syndrome.

AB - Cornelia de Lange syndrome involves anomalies in cardio-vascular and musculo-skeletal systems, and mental retardation. In addition, a patient with this syndrome shows a peculiar look. A 22-year-old woman with Cornelia de Lange syndrome underwent general anesthesia twice. She has a small mouth, thin lips, a short neck, short limbs, and stiffness of the neck and some joints associated with slight mental retardation. She was scheduled for arthroscopy and then for rotational acetabular osteotomy and valgus osteotomy. The maximum distance between the upper and lower incisors was 34 mm, when she opened her mouth. Anesthesia was induced with sevoflurane increased slowly to 7.0% in oxygen 6 l · min-1 in both procedures. After the administration of 4% lidocaine 3.5ml into the pharynx, orotracheal intubation was attempted, but was not successful. Then blind naso-tracheal intubation was performed successfuly under spontaneous respiration under sevoflurane-oxygen inhalation. The induction of anesthesia with sevoflurane under spontaneous respiration was useful for blind naso-tracheal intubation in a case with difficult intubation such as in Cornelia de Lange syndrome.

UR - http://www.scopus.com/inward/record.url?scp=0033913335&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=0033913335&partnerID=8YFLogxK

M3 - Article

C2 - 10933036

AN - SCOPUS:0033913335

VL - 49

SP - 786

EP - 787

JO - Japanese Journal of Anesthesiology

JF - Japanese Journal of Anesthesiology

SN - 0021-4892

IS - 7

ER -