Hepatic nodular hyperplasia in a boy with Alagille syndrome: CT and MR appearances

Tsuyoshi Tajima, Hiroshi Honda, Katsuhiko Yanaga, Toshirou Kuroiwa, Kengo Yoshimitsu, Hiroyuki Irie, Yasuo Kuwabara, Kenichi Taguchi, Kouji Masuda

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    Abstract

    A boy with Alagille syndrome complicated by hepatic nodular hyperplasia (HNH) is reported. During pre-transplantation evaluation, CT and MRI revealed a large hepatic lesion with multiple small nodular lesions. Angiography demonstrated a large hypervascular lesion and CT arterial portography (CTAP) showed a portal perfusion defect corresponding to the lesion. CTAP also revealed large portal vein branches running through the lesion. Although hepatocellular carcinoma is known to accompany Alagille syndrome, HNH should also be considered when large vessels running through the lesion are demonstrated.

    Original languageEnglish
    Pages (from-to)584-588
    Number of pages5
    JournalPediatric Radiology
    Volume31
    Issue number8
    DOIs
    Publication statusPublished - Jan 1 2001

    All Science Journal Classification (ASJC) codes

    • Pediatrics, Perinatology, and Child Health
    • Radiology Nuclear Medicine and imaging

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  • Cite this

    Tajima, T., Honda, H., Yanaga, K., Kuroiwa, T., Yoshimitsu, K., Irie, H., Kuwabara, Y., Taguchi, K., & Masuda, K. (2001). Hepatic nodular hyperplasia in a boy with Alagille syndrome: CT and MR appearances. Pediatric Radiology, 31(8), 584-588. https://doi.org/10.1007/s002470100510