Holocord hydrosyringomyelia with terminal myelocystocele revealed by constructive interference in steady-state MR imaging

Kimiaki Hashiguchi, Takato Morioka, Kazuhiro Samura, Fumiaki Yoshida, Yasushi Miyagi, Shinji Nagata, Takayuki Kokubo, Takashi Yoshiura, Tomio Sasaki

Research output: Contribution to journalArticlepeer-review

7 Citations (Scopus)

Abstract

We report an operated case with terminal myelocystocele and holocord hydrosyringomyelia (syrinx). The patient exhibited a subcutaneous mass at the right lumbosacral region with multiple anomalies including scoliosis and hyperdactylia of the right foot and systemic disease such as hydronephroureter. Neurological examination revealed palsy of the left diaphragm, and left upper and right lower limbs. Constructive interference in steady-state (CISS) images demonstrated a terminal myelocystocele with a huge syrinx extending to the medulla. The curvilinear reconstruction of the CISS sequence depicted continuous cystocele and whole syrinx. At day 37, sac excision and untethering of the spinal cord were performed. The caudal part of the central canal was opened to the subarachnoid space (terminal ventriculostomy), resulting in a slight improvement of limb palsy and shrinkage of the holocord syrinx. CISS imaging is useful to detect the complicated pathology, and terminal ventriculostomy should be performed to improve associated syrinx.

Original languageEnglish
Pages (from-to)509-512
Number of pages4
JournalPediatric Neurosurgery
Volume44
Issue number6
DOIs
Publication statusPublished - Jan 2009

All Science Journal Classification (ASJC) codes

  • Pediatrics, Perinatology, and Child Health
  • Surgery
  • Clinical Neurology

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