Living donor liver transplantation for an infant with osteogenesis imperfecta and intrahepatic cholestasis: Report of a case

Young Rok Choi, Nam Joon Yi, Jae Sung Ko, Jung Min Ko, Ung Sik Jin, Hee Soo Kim, Kook Hyun Lee, Tae Joon Cho, Suk Won Suh, Tae Yoo, Kwang Woong Lee, Kyung Suk Suh

Research output: Contribution to journalArticlepeer-review

2 Citations (Scopus)

Abstract

Osteogenesis imperfecta (OI) is a group of genetic disorders characterized by bone fragility and connective tissue manifestations. We report a successful liver transplantation (LT) in an 8-month-old boy with OI and cholestatic biliary cirrhosis. After 4 cycles of intravenous pamidronate, LT was performed under intravenous anesthesia using a left lateral section from his mother without mechanical retractors. The operation time was 420 min and estimated blood loss was 520 mL requiring one unit of RBC transfusion. He was discharged without surgical complications. Therefore, LT should be considered for patients with end stage liver disease and OI under organic multidisciplinary cooperation.

Original languageEnglish
Pages (from-to)441-444
Number of pages4
JournalJournal of Korean Medical Science
Volume29
Issue number3
DOIs
Publication statusPublished - 2014

All Science Journal Classification (ASJC) codes

  • Medicine(all)

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