Perioperative management of a patient with Bernard-Soulier syndrome that has a refractoriness to platelet transfusion

D. Yoshiga, A. Yoshida, S. Kitahara, C. Harada, Shinichi Ito, Seiji Nakamura, K. Kubo

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

A patient with Bernard-Soulier syndrome (BSS), characterized by extremely large platelets, thrombocytopenia and prolonged bleeding time underwent general anesthesia for platelet adhesion aberration. This patient has developed a refractoriness to platelet transfusion due to a frequent transfusion of platelets; however the operation was completed without abnormal bleeding by transfusing HLA-matched platelets during the procedure. BSS is a very rare syndrome so there are no well-defined protocols for the management of perioperative bleeding associated with this syndrome. In this report, we present the detail of the perioperative management for these patients with BSS who has a refractoriness to platelet transfusion.

Original languageEnglish
Pages (from-to)102-104
Number of pages3
JournalAsian Journal of Oral and Maxillofacial Surgery
Volume23
Issue number2
DOIs
Publication statusPublished - May 1 2011

All Science Journal Classification (ASJC) codes

  • Surgery
  • Oral Surgery
  • Orthopedics and Sports Medicine

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