Pulmonary capillary hemangiomatosis with severe pulmonary hypertension

Koji Ito, Toshihiro Ichiki, Keiji Ohi, Kensuke Egashira, Mituhiko Ohta, Kenichi Taguchi, Akira Takeshita

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23 Citations (Scopus)

Abstract

Pulmonary capillary hemangiomatosis (PCH) is a rare idiopathic lung disorder that occurs in young patients and leads to pulmonary hypertension (PH). It is difficult to diagnosis in the early stage and is often mistaken for primary PH; in almost all cases of PCH, the correct diagnosis is not made until autopsy. In the present case of PCH, the patient had severe pulmonary hypertension and died of respiratory failure. Pathologically, PCH is characterized by proliferation of benign thin-walled capillary sized blood vessels in the lung parenchyma.

Original languageEnglish
Pages (from-to)793-795
Number of pages3
JournalCirculation Journal
Volume67
Issue number9
DOIs
Publication statusPublished - Sep 1 2003

All Science Journal Classification (ASJC) codes

  • Cardiology and Cardiovascular Medicine

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    Ito, K., Ichiki, T., Ohi, K., Egashira, K., Ohta, M., Taguchi, K., & Takeshita, A. (2003). Pulmonary capillary hemangiomatosis with severe pulmonary hypertension. Circulation Journal, 67(9), 793-795. https://doi.org/10.1253/circj.67.793