Pulmonary capillary hemangiomatosis with severe pulmonary hypertension

Koji Ito, Toshihiro Ichiki, Keiji Ohi, Kensuke Egashira, Mituhiko Ohta, Kenichi Taguchi, Akira Takeshita

    Research output: Contribution to journalArticlepeer-review

    24 Citations (Scopus)


    Pulmonary capillary hemangiomatosis (PCH) is a rare idiopathic lung disorder that occurs in young patients and leads to pulmonary hypertension (PH). It is difficult to diagnosis in the early stage and is often mistaken for primary PH; in almost all cases of PCH, the correct diagnosis is not made until autopsy. In the present case of PCH, the patient had severe pulmonary hypertension and died of respiratory failure. Pathologically, PCH is characterized by proliferation of benign thin-walled capillary sized blood vessels in the lung parenchyma.

    Original languageEnglish
    Pages (from-to)793-795
    Number of pages3
    JournalCirculation Journal
    Issue number9
    Publication statusPublished - Sep 1 2003

    All Science Journal Classification (ASJC) codes

    • Cardiology and Cardiovascular Medicine


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