Repeated anesthesia management in a patient with aicardi syndrome

Takashi Hitosugi, Masanori Tsukamoto, Kentaro Ishii, Masanori Kadowaki, Shigeki Fujiwara, Takeshi Yokoyama

Research output: Contribution to journalArticle

Abstract

Aicardi syndrome is a rare hereditary disorder that develops in only girls with the trilogy of nutatory epilepsy, callosal agenesis and chorioretinopathy. We experienced general anesthesia twice for a patient with Aicardi syndrome in addition to heavy mental retardation. She underwent surgical correction for cleft lip and palate at 6 months of age and at 2 years of age, respectively. Anesthesia was induced slowly with inhalation of nitrous oxide, oxygen and sevoflurare. After securing an intravenous route, midazolam, thiopental and vecuronium were administered and intubated orally. Anesthesia was maintained with isoflurane safely. Patients with Aicardi syndrome have a high risk of aspiration pneumonia caused by underdeveloped swallowing ability due to callosal agenesis. We should, therefore, pay attention to prevention of seizure and aspiration pneumonia during the perioperative period.

Original languageEnglish
Pages (from-to)78-81
Number of pages4
JournalJapanese Journal of Anesthesiology
Volume65
Issue number1
Publication statusPublished - Jan 1 2016

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Aicardi Syndrome
Agenesis of Corpus Callosum
Aspiration Pneumonia
Anesthesia
Vecuronium Bromide
Perioperative Period
Aptitude
Thiopental
Cleft Lip
Isoflurane
Midazolam
Nitrous Oxide
Cleft Palate
Deglutition
Intellectual Disability
General Anesthesia
Inhalation
Epilepsy
Seizures
Oxygen

All Science Journal Classification (ASJC) codes

  • Anesthesiology and Pain Medicine

Cite this

Repeated anesthesia management in a patient with aicardi syndrome. / Hitosugi, Takashi; Tsukamoto, Masanori; Ishii, Kentaro; Kadowaki, Masanori; Fujiwara, Shigeki; Yokoyama, Takeshi.

In: Japanese Journal of Anesthesiology, Vol. 65, No. 1, 01.01.2016, p. 78-81.

Research output: Contribution to journalArticle

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