Rudimentary Meningocele

We report a 6-year-old boy with rudimentary meningocele (RMC) on the midline of the occipital area since birth. To the best of our knowledge, only 9 cases of RMC have been reported in Japan. RMC has been reported as a variant of primary cutaneous meningioma, but has recently been described as a histologically isolated entity. Some reports have referred to bone defects beneath the lesion and a connection with the underlying dural tissue through the defect. Therefore, a careful preoperative evaluation, including imaging studies such as computed tomography or magnetic resonance image, to rule out the possibility of a lesion being RMC, whenever we encounter an infant or a child presenting with a midline lesion of the scalp, such as a nodule or an alopecia.