TY - JOUR
T1 - TUBEROUS SCLEROSIS WITH PULMONARY AND LYMPH NODE INVOLVEMENT
T2 - Relationship to Lymphangiomyomatosis
AU - KAKU, Tsimehisa
AU - TOYOSHIMA, Satoshi
AU - ENJOJI, Munetomo
PY - 1983/3
Y1 - 1983/3
N2 - A rare case of classical tuberous sclerosis complex with pulmonary and lymph node involvement is presented. The lungs showed small cysts or honeycombing associated with smooth muscle proliferation in the walls of bronchioles, blood vessels, lymphatics, and alveolar septa. In the enlarged mediastinal and retroperitoneal lymph nodes, the normal structure was replaced by interlacing bundles of proliferated smooth muscle cells. These features were consistent with those of lymphangiomyomatosis. The close relationship between tuberous sclerosis and lymphangiomyomatosis is discussed. ACTA PATHOL. JPN. 33: 395–401, 1983.
AB - A rare case of classical tuberous sclerosis complex with pulmonary and lymph node involvement is presented. The lungs showed small cysts or honeycombing associated with smooth muscle proliferation in the walls of bronchioles, blood vessels, lymphatics, and alveolar septa. In the enlarged mediastinal and retroperitoneal lymph nodes, the normal structure was replaced by interlacing bundles of proliferated smooth muscle cells. These features were consistent with those of lymphangiomyomatosis. The close relationship between tuberous sclerosis and lymphangiomyomatosis is discussed. ACTA PATHOL. JPN. 33: 395–401, 1983.
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U2 - 10.1111/j.1440-1827.1983.tb01426.x
DO - 10.1111/j.1440-1827.1983.tb01426.x
M3 - Article
C2 - 6869006
AN - SCOPUS:0020563828
SN - 1320-5463
VL - 33
SP - 395
EP - 401
JO - Acta Pathologica Japonica
JF - Acta Pathologica Japonica
IS - 2
ER -