Anesthetic management for a pediatric patient of Klippel-Trenaunay syndrome with giant head by hydrocephalus

Hiroshi Hoshijima, Risa Takeuchi, Masanori Tsukamoto, Saori Ogawa, Yoshinori Iwase, Nobuyuki Matsumoto

研究成果: ジャーナルへの寄稿記事

2 引用 (Scopus)

抄録

Klippel-Trenaunay syndrome (KTS) is a rare disorder associated with the triad of 1) capillary vascular malformation, 2) varicose veins and/or venous malformation, 3) and soft tissue and/or bony hypertrophy. A six-month old, 6.0-kg-weight male pediatric patient was scheduled for ventriculo-peritoneal shunt operation for hydrocephalus caused by obstructive aqueductus cerebri. At the age of three months, he was diagnosed as KTS by extensive capillary vascular malformation and soft tissue hypertrophy of the right leg. Physical examination showed prominent vascular malformation over his anterior thoracic and abdominal wall, and soft tissue hypertrophy was only on his right leg. Simultaneously, he was complicated with congenital hydrocephalus because of obstructive aqueductus cerebri. His head and skull were enlarged and his head measurement reached 55 cm (chest measurement 32 cm). Anesthetic management of KTS patients should be prepared with blood transfusion against massive hemorrhage and hypovolemic shock. Furthermore, KTS patients should be always considered to have airway difficulty due to the soft tissue hypertrophy, upper and airway hemangiomas. Therefore, we planned safer tracheal intubation following practice guidelines for management of the difficult airway.

元の言語英語
ページ(範囲)1356-1358
ページ数3
ジャーナルJapanese Journal of Anesthesiology
61
発行部数12
出版物ステータス出版済み - 12 1 2012
外部発表Yes

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Klippel-Trenaunay-Weber Syndrome
Hydrocephalus
Hypertrophy
Vascular Malformations
Anesthetics
Cerebral Aqueduct
Head
Pediatrics
Leg
Ventriculoperitoneal Shunt
Practice Management
Varicose Veins
Abdominal Wall
Thoracic Wall
Hemangioma
Practice Guidelines
Intubation
Skull
Blood Transfusion
Physical Examination

All Science Journal Classification (ASJC) codes

  • Anesthesiology and Pain Medicine

これを引用

Anesthetic management for a pediatric patient of Klippel-Trenaunay syndrome with giant head by hydrocephalus. / Hoshijima, Hiroshi; Takeuchi, Risa; Tsukamoto, Masanori; Ogawa, Saori; Iwase, Yoshinori; Matsumoto, Nobuyuki.

:: Japanese Journal of Anesthesiology, 巻 61, 番号 12, 01.12.2012, p. 1356-1358.

研究成果: ジャーナルへの寄稿記事

Hoshijima, H, Takeuchi, R, Tsukamoto, M, Ogawa, S, Iwase, Y & Matsumoto, N 2012, 'Anesthetic management for a pediatric patient of Klippel-Trenaunay syndrome with giant head by hydrocephalus', Japanese Journal of Anesthesiology, 巻. 61, 番号 12, pp. 1356-1358.
Hoshijima, Hiroshi ; Takeuchi, Risa ; Tsukamoto, Masanori ; Ogawa, Saori ; Iwase, Yoshinori ; Matsumoto, Nobuyuki. / Anesthetic management for a pediatric patient of Klippel-Trenaunay syndrome with giant head by hydrocephalus. :: Japanese Journal of Anesthesiology. 2012 ; 巻 61, 番号 12. pp. 1356-1358.
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