Anesthetic management of a patient with Williams syndrome

研究成果: ジャーナルへの寄稿記事

抄録

A 9-year-old boy with Williams syndrome was scheduled to receive dental treatment under general anesthesia. He had been diagnosed as having Williams syndrome based on the presence of characteristic features, including an elfin face, mental retardation, and congenital supravalvular aortic stenosis and hypercalcemia. Airway management using a mask technique was easily performed. Anesthesia was induced slowly with the inhalation of oxygen and sevoflurane. After obtaining an intravenous route, fentanyl and rocuronium were administered and the patient was intubated nasally. Tracheal intubation (using an Airway Scope®) was performed. The anesthesia was safely maintained using sevoflurane. Patients with Williams syndrome have a high risk of sudden death caused by arrhythmias or cardiac arrest. Therefore, special care to prevent heart failure during the perioperative period using a noninvasive hemodynamic monitor and appropriate management of the circulatory system, mental retardation, malignant hyperthermia, and hypercalcemia is needed in patients with this syndrome.

元の言語英語
ページ(範囲)150-152
ページ数3
ジャーナルJournal of Japanese Dental Society of Anesthesiology
44
発行部数2
出版物ステータス出版済み - 2016

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Williams Syndrome
Anesthetics
Hypercalcemia
Intellectual Disability
Anesthesia
Supravalvular Aortic Stenosis
Malignant Hyperthermia
Perioperative Period
Airway Management
Fentanyl
Masks
Cardiovascular System
Sudden Death
Heart Arrest
Intubation
General Anesthesia
Inhalation
Cardiac Arrhythmias
Tooth
Heart Failure

All Science Journal Classification (ASJC) codes

  • Anesthesiology and Pain Medicine
  • Dentistry(all)

これを引用

Anesthetic management of a patient with Williams syndrome. / Hitosugi, Takashi; Tsukamoto, Masanori; Shiba, Rika; Koyama, Sayuri; Yokoyama, Takeshi.

:: Journal of Japanese Dental Society of Anesthesiology, 巻 44, 番号 2, 2016, p. 150-152.

研究成果: ジャーナルへの寄稿記事

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