Liver failure caused by hepatic angiodysplasia in hereditary hemorrhagic telangiectasia

Chizu Mukasa, Kazuhiko Nakamura, Yoshiharu Chijiiwa, Hironori Sakai, Hajime Nawata

研究成果: ジャーナルへの寄稿記事

9 引用 (Scopus)

抄録

Hereditary hemorrhagic telangiectasia is a systemic vascular disease with autosomal dominant inheritance that results in telaugiectasia, arteriovenous malformations, and hemangiomas. The liver is one of the organs commonly affected in hereditary hemorrhagic telangiectasia, and hepatic lesions consist of angiodysplasia and fibrosis. A patient with hereditary hemorrhagic telangiectasia and significant impairment of synthetic liver function is reported. Dynamic computed tomography revealed marked enlargement of the common hepatic and intrahepatic arteries, heterogeneous parenchymography, and early opacification of the hepatic veins consistent with telangiectasias and arteriovenous shunting. Overall, the liver was predominantly occupied by vascular structures and scarce residual hepatic parenchyma. Other causes of liver dysfunction, such as viral hepatitis and alcohol abuse, were excluded. In general, hepatic fibrovascular dysplasia seen in hereditary hemorrhagic telangiectasia usually results in only mild liver dysfunction; however, this case shows that hepatic involvement may rarely result in hepatic failure.

元の言語英語
ページ(範囲)471-473
ページ数3
ジャーナルAmerican Journal of Gastroenterology
93
発行部数3
DOI
出版物ステータス出版済み - 1 1 1998

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Angiodysplasia
Hereditary Hemorrhagic Telangiectasia
Liver Failure
Liver
Liver Diseases
Telangiectasis
Hepatic Veins
Arteriovenous Malformations
Hepatic Artery
Hemangioma
Vascular Diseases
Hepatitis
Alcoholism
Blood Vessels
Fibrosis
Tomography

All Science Journal Classification (ASJC) codes

  • Hepatology
  • Gastroenterology

これを引用

Liver failure caused by hepatic angiodysplasia in hereditary hemorrhagic telangiectasia. / Mukasa, Chizu; Nakamura, Kazuhiko; Chijiiwa, Yoshiharu; Sakai, Hironori; Nawata, Hajime.

:: American Journal of Gastroenterology, 巻 93, 番号 3, 01.01.1998, p. 471-473.

研究成果: ジャーナルへの寄稿記事

Mukasa, Chizu ; Nakamura, Kazuhiko ; Chijiiwa, Yoshiharu ; Sakai, Hironori ; Nawata, Hajime. / Liver failure caused by hepatic angiodysplasia in hereditary hemorrhagic telangiectasia. :: American Journal of Gastroenterology. 1998 ; 巻 93, 番号 3. pp. 471-473.
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