Neurosurgical management of occult spinal dysraphism associated with OEIS complex

Takato Morioka, Kimiaki Hashiguchi, Fumiaki Yoshida, Kenichi Matsumoto, Yasushi Miyagi, Shinji Nagata, Takashi Yoshiura, Kouji Masumoto, Tomoaki Taguchi, Tomio Sasaki

研究成果: Contribution to journalArticle査読

15 被引用数 (Scopus)

抄録

Introduction: OEIS complex has been described as a combination of defects consisting of o mphalocele (O), e xstrophy of the cloaca (E), imperforate anus (I), and s pinal defects (S). As the first three defects are life-threatening and treated on a priority basis, neurosurgical intervention for spinal defects is deferred until recuperation from abdominogenital repair. However, the best timing for neurosurgical operation has not been precisely described. Materials and methods: We reviewed our neurosurgical management of three cases (case 1: myelomeningocele; cases 2 and 3: terminal myelocystocele). At 2-6 (3.6 on average) months after birth, neurosurgical procedures, including reduction of the size of the lumbosacral cystic lesion and untethering of the spinal cord, were performed. Results: During this period, the patients' weights increased from 1,911 to 3,368 g on average, and the lumbosacral cystic lesion was markedly enlarged. In all cases, no neurological deterioration was seen, and ventriculoperitoneal shunt was not indicated. Conclusion: Thus, neurosurgical procedures can be performed in patients weighing 3-4 kg and/or at an age of 3 months, after confirming recuperated conditions from abdominogenital repair. Careful observation should be made of the size of the lumbosacral cystic lesion and neurological deterioration.

本文言語英語
ページ(範囲)723-729
ページ数7
ジャーナルChild's Nervous System
24
6
DOI
出版ステータス出版済み - 6 2008

All Science Journal Classification (ASJC) codes

  • 小児科学、周産期医学および子どもの健康
  • 臨床神経学

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